Partial unilateral lentiginosis with ocular involvement

Partial unilateral lentiginosis (PUL) is an unusual pigmentary disorder cha racterized by numerous lentigines grouped within an area of normal skin; th e pigmented macules are often in a segmental distribution with a sharp dema rcation at the midline. We report the first case of ocular involvement in a patient with this diagnosis. The patient, a 30-year-old Peruvian woman, ha d multiple brown macules on the left upper Face in primarily a V1 and V2 di stribution with a sharp demarcation at the midline of the forehead. The les ions first appeared near the hairline when she was 5 years of age, and then began to extend onto the face. She also had a discrete area of brown pigme ntation on the left lateral bulbar conjunctiva. Because the patient had bee n previously diagnosed by several dermatologists as having either a speckle d lentiginous nevus or a nevus of Ota, we draw attention to the entity PUL and the possibility of ocular involvement.