Aortitis is the inflammation of the wall of the aorta and can occur from an
infection or autoimmune disease. Myelodysplastic syndrome (MDS) is charact
erised by abnormal haematopoiesis and a dysfunctional immune system. Autoim
mune manifestations have been described in MDS. Here a case of a patient wi
th aortitis and MDS is presented and discussed. All possible aetiologies we
re ruled out. The patient's symptoms resolved after she received steroids.