Diagnostic criteria of the syndrome of atypical benign partial childhood epilepsy

The paper presents an analysis of clinical-neuropsychological peculiarities of the syndrome of atypical benign partial childhead epilepsy (pseudolenno x syndrome) of 6 patients (3 boys, 3 girls). An age of the onset of the dis ease was between 1,5-4 years. There was polymorphism of paroxysms, their hi gh frequency with an obligate presence of hemifacial fits and atypical abse nces. Night generalized tonic-clonic attacks and the falling attacks were f ound in 67% of the patients. Spectrum of the neurological disorders include d disorders of speech and a slight cerebella symptomatology. Regional <<rol andic>> activity and diffuse epileptiformed disorders, increasing into a ph ase of a slow sleep, were registered by EEC. Resistance to anticonvulsive t herapy was revealed. The authors had demonstrated a nosologic independence of pseudolennox syndrome and had considered worth while to pick it out in a group of cryptogenic partial forms of epilepsy together with the epileptic aphasia of Landau-Kleffner and an epilepsy with the continuous peak-waves during the slow sleep.