Cavopulmonary connection after repair of pulmonary vein stenoses

We report a case of heterotaxia with single-ventricle physiology undergoing successively pulmonary artery banding (PAB) at 8 months of age, repair of pulmonary vein (PV) stenoses at 15 months of age, and a fenestrated total c avopulmonary connection (TCPC) combined with repair of a regurgitant common atrioventricular (AV) valve and a Damus-Stansel operation for a restrictiv e subaortic ventricle at 5 years of age, followed by percutaneous closure o f the fenestration. The child is now 10 years old and is, to the best of ou r knowledge, the only reported long-term survivor of a Fontan type procedur e done after repair of PV stenoses. (C) 2001 by The Society of Thoracic Sur geons.