Km. Uysal et al., A rare tumor of craniofacial bones in children: A pediatric chondroblasticosteosarcoma case with diagnostic and therapeutic problems, PED HEM ONC, 18(2), 2001, pp. 147-152
Osteosarcoma of the cranial facial region is uncommon and only rarely invol
ves the ethmoid or sphenoid bones. The authors report on an unusual case of
a 17-year-old male presenting with chondroblastic osteosarcoma of the maxi
llary, ethmoid, and sphenoid sinuses who remains well and disease-free at 4
6 months. He was treated with anterior craniofacial resection followed by p
ostoperative radiotherapy to the sight of the primary tumor. He did not rec
eive chemotherapy because of emerging hepatitis-B infection and vasculitis.
The literature on extragnathic craniofacial osteosarcomas is reviewed with
particular emphasis on treatment options of this rare tumor.