A rare tumor of craniofacial bones in children: A pediatric chondroblasticosteosarcoma case with diagnostic and therapeutic problems

Osteosarcoma of the cranial facial region is uncommon and only rarely invol ves the ethmoid or sphenoid bones. The authors report on an unusual case of a 17-year-old male presenting with chondroblastic osteosarcoma of the maxi llary, ethmoid, and sphenoid sinuses who remains well and disease-free at 4 6 months. He was treated with anterior craniofacial resection followed by p ostoperative radiotherapy to the sight of the primary tumor. He did not rec eive chemotherapy because of emerging hepatitis-B infection and vasculitis. The literature on extragnathic craniofacial osteosarcomas is reviewed with particular emphasis on treatment options of this rare tumor.