FIBROSARCOMA IN CHILDREN - A RARE TUMOR WITH LONG-TERM SURVIVAL EVEN WITH ADVANCED DISEASE - A REPORT OF 3 CASES

Fibrosarcoma is a rare tumour in children. The potential of malignancy has been questioned. We present three cases of fibrosarcoma in childr en. The follow-up periods range from 10 to 37 years. The first patient had pulmonary metastases at the time of diagnosis in 1958. The primar y tumour in fossa ischio-rectalis was resected in 1960. Lung metastase s were resected in 1960 and 1989. Radiotherapy was given in 1992. He i s still alive with metastases 37 years after the first manifestation o f disease. The second patient had a primary tumour and several local r ecurrences in the mandible. He is alive without evidence of disease 4 years after resection of pulmonary metastases and 21 years after resec tion of the primary tumour. The third patient has no signs of recurren ce or metastasic spread 10 years after a wide excision of subcutanous tumours of the left upper arm. The cases demonstrate a special tumour- entity of low-grade malignancy, which show a good prognosis and a wide spectrum of biological behaviour.