Purpose. Our objective was to describe characteristic contrast enema f
indings of fibrosing colonopathy. Materials and methods. We performed
barium enemas on 18 children with cystic fibrosis who had received gre
ater than 4500 U of lipase per kg body weight per meal and who had dis
tal intestinal obstruction syndrome unresponsive to medical management
. Results. Fifteen patients had abnormal enema results. The most commo
n findings included structure, loss of haustra, and colonic shortening
. Ten patients required surgery, nine underwent colon resection, and o
ne had lysis of adhesions. Pathologists confirmed fibrosing colonopath
y in eight of nine specimens. Conclusion. Colonic structure, abnormal
haustra, and longitudinal shortening are characteristic barium enema f
indings of fibrosing colonopathy.