A CASE OF INFANTILE DUBIN-JOHNSON-SYNDROME WITH HIGH CT ATTENUATION IN THE LIVER

We report a case of Du bin-Johnson syndrome (DJS) with severe infantil e cholestasis and elevated computed tomography (CT) attenuation of the liver. Increased levels of urinary coproporphyrin I were found as wel l as pigment granules in the hepatocytes and hepatosteatosis. The CT a ttenuation was markedly higher in the liver of this patient at the age s of 3 and 7 months than in the spleen or kidneys. This high attenuati on may be a finding specific to infantile DJS and, therefore, abdomina l CT may be helpful in the diagnosis.