We present a case of persistent right umbilical vein with Noonan's syndrome
. Persistence of the right umbilical vein with no intrahepatic portion is a
n uncommon finding with a review of the literature revealing only five othe
r cases. In these cases drainage was directly into the right atrium, inferi
or vena cava (IVC) or IVC via the iliac vein. Of the reported cases Noonan'
s syndrome was confirmed in one case and suspected in a second. This report
represents a third case of persistent right umbilical vein with confirmed
Noonan's syndrome.