FREEMAN-SHELDON (WHISTLING FACE) SYNDROME - ANESTHETIC AND AIRWAY MANAGEMENT

We describe the anaesthetic management of Freeman-Sheldon syndrome in a two-and-a-half year old undergoing club foot correction. Following a n inhalational induction using halothane, tracheal intubation by direc t laryngoscopy proved impossible. A laryngeal mask airway was inserted and intubation with a 4.5 tracheal tube was successfully achieved usi ng a fibreoptic bronchoscope passed through the LMA. The child had an uneventful anaesthetic course. A caudal epidural was used for postoper ative analgesia and the child was discharged home on day two. The anae sthetic and airway management options of this syndrome are outlined.