M. Jahangiri et al., Long-term results of relief of subaortic stenosis in univentricular atrioventricular connection with discordant ventriculoarterial connections, ANN THORAC, 71(3), 2001, pp. 907-910
Citations number
7
Categorie Soggetti
Cardiovascular & Respiratory Systems","Medical Research Diagnosis & Treatment
Background. We set out to examine the long-term results of relief of subaor
tic stenosis by enlargement of ventricular septal defect in patients with u
niventricular atrioventricular connection to a dominant left ventricle and
discordant ventriculoarterial connections.
Methods. Twenty-four patients underwent enlargement of ventricular septal d
efect between 1985 and 1998 at a median age of 3.2 years (range, 3 weeks to
14 years). Ten patients were younger than 1 year of age. Eighteen had unde
rgone previous banding of the pulmonary trunk, 9 of whom also required repa
ir of coarctation of the aorta. The median subaortic gradient before enlarg
ement was 46 mm Hg. Twenty-three patients had a patch to enlarge the rudime
ntary right ventricle.
Results. Five patients (21%) died in the early postoperative period. The ov
erall survival at 1 and 3 years was 73%, and at 5 and 10 years was 68% and
60%, respectively. Complete heart block requiring insertion of a pacemaker
occurred in 2 patients (8%). A Fontan operation was performed in 10 patient
s, 5 underwent a bidirectional Glenn procedure, and 2 required cardiac tran
splantation. Follow-up was complete in all survivors at a median time of 6.
7 years (range, 8 months to 13 years). From the earlier part of the series,
3 patients experienced aortic insufficiency and 2 had recurrent obstructio
n. Factors adversely affecting survival were age younger than 1 year at ope
ration and presence of obstruction within the aortic arch.
Conclusions. Our experience shows that, in patients with univentricular atr
ioventricular connection to a dominant left ventricle and subaortic stenosi
s, enlargement of the ventricular septal defect provides satisfactory relie
f of obstruction except in those younger than 1 year of age, and those who
have associated obstruction in the aortic arch. (C) 2001 by The Society of
Thoracic Surgeons.