Antenatal sonographic findings of right pulmonary agenesis with ipsilateral microtia: a possible new laterality association

Right pulmonary agenesis is a rare congenital malformation which results in secondary dextrocardia in situs solitus. Ipsilateral microtia in this cont ext composes a laterality syndrome. The prenatal sonographic findings of th is abnormality have not been previously reported. We describe the associati on of dextrocardia in situs solitus, intact diaphragm and right microtia. T his was sonographically diagnosed at mid-gestation in an euploid fetus. Sur gical evacuation of the pregnancy confirmed the external malformation. Late rality association should be assessed in a fetus with sonographic findings of pulmonary agenesis. The differential diagnosis and updated literature re view is presented. Copyright (C) 2001 John Wiley & Sons, Ltd.