Spontaneous common iliac arteries rupture in Ehlers-Danlos syndrome type IV: report of two cases and review of the literature

Authors
Habib, K Memon, MA Reid, DA Fairbrother, BJ
Citation
K. Habib et al., Spontaneous common iliac arteries rupture in Ehlers-Danlos syndrome type IV: report of two cases and review of the literature, ANN RC SURG, 83(2), 2001, pp. 96-104
Citations number
61
Categorie Soggetti
Surgery
Journal title
ANNALS OF THE ROYAL COLLEGE OF SURGEONS OF ENGLAND
ISSN journal
00358843 → ACNP
Volume
83
Issue
2
Year of publication
2001
Pages
96 - 104
Database
ISI
SICI code
0035-8843(200103)83:2<96:SCIARI>2.0.ZU;2-4
Abstract
Two patients with previously undiagnosed Ehlers-Danlos syndrome type IV (ED S IV) presented acutely with clinical features suggestive of hypovolemic sh ock. Emergency laparotomies in both of them revealed spontaneous rupture of the common iliac arteries. The clinical features, operative findings, surg ical approach, outcome and implications are discussed.