We report a 13-year-old boy suffering from severe ichthyosis linearis circu
mflexa. Evidence of hair shaft abnormalities and impaired immunity could no
t be found. The patient was treated with salt water baths and artificial UV
B radiation (balneophototherapy) 3-5 times weekly. After 40 treatments with
balneophototherapy the skin lesions were almost completely cleared and mai
ntenance UVB monotherapy was performed twice weekly for 2 months. After 4 m
onths, however, the disease relapsed. Balneophototherapy presents a potenti
ally effective and well tolerated phototherapeutic option for ichthyosis li
nearis circumflexa. As only short periods of remission may be expected, int
ermittent balneophototherapy would be probably necessary to control the dis
ease.