Congenital pulmonary fibrosarcoma. Differential diagnosis of infantile pulmonary spindle-cell tumors

Primary pulmonary mesenchymal tumors are rare causes of intrathoracic lesio ns in newborns. We describe a case of pulmonary spindle-cell tumor with fea tures of infantile fibrosarcoma and discuss the differential diagnosis of s pindle-cell lesions in this location In view of further case reports of the literature,this neoplasia can best be categorized in a spectrum of fibrobl astic/myofibroblastic differentiated spindle-cell tumors, with excellent pr ognosis. Especially in congenital lesions a favorable clinical course is to be expected after complete surgical resection. Additional radio- and/or ch emotherapy is not recommended.