Lymphangioma circumscriptum of the vulva

Lymphangioma circumscriptum is a benign disease of the lymph ducts and an u nusual pathologic process that rarely affects the vulva. The etiology of th is lesion is not clear, but obstruction of the lymph vessels has been sugge sted as a possible cause in some cases. We report the case of a 44-year-old woman with lesions similar to lymphangioma circumscriptum of the vulva and chronic idiopathic lymphedema of the lower right limb. Because there was n o obvious cause, we propose that the lymphangioma was caused by the lymphed ema.