Moyamoya disease complicated with renal artery stenosis and nephrotic syndrome: Reversal of nephrotic syndrome after nephrectomy

Authors
Kuwayama, F Hamasaki, Y Shinagawa, T Kubota, C Ichikawa, I Kato, Y Oi, S Shinohara, O
Citation
F. Kuwayama et al., Moyamoya disease complicated with renal artery stenosis and nephrotic syndrome: Reversal of nephrotic syndrome after nephrectomy, J PEDIAT, 138(3), 2001, pp. 418-420
Citations number
14
Categorie Soggetti
Pediatrics,"Medical Research General Topics
Journal title
JOURNAL OF PEDIATRICS
ISSN journal
00223476 → ACNP
Volume
138
Issue
3
Year of publication
2001
Pages
418 - 420
Database
ISI
SICI code
0022-3476(200103)138:3<418:MDCWRA>2.0.ZU;2-6
Abstract
A 7-year-old boy with moyamoya disease developed sustained hypertension, ne phrotic syndrome, hyperreninemia, and occlusion of the right renal artery. After right nephrectomy, hyperreninemia and hypertension improved. Proteinu ria was resolved after nephrectomy, in parallel with the decrease in plasma renin activity. Moyamoya disease can cause nephrotic-range proteinuria, wh ich is caused hemodynamically by hyperreninemia.