Cc. Liang et al., PRENATAL-DIAGNOSIS OF TETRALOGY OF FALLOT WITH ABSENT PULMONARY VALVEACCOMPANIED BY HYDROPS-FETALIS, Gynecologic and obstetric investigation, 44(1), 1997, pp. 61-63
Tetralogy of Fallot with absent pulmonary valve is a rare congenital c
ardiac anomaly. We report on the echocardiographic features of a fetus
with such an anomaly and aneurysm of the pulmonary artery associated
with hydrops fetalis and polyhydramnios. The prognosis of tetralogy of
Fallot with absent pulmonary valve and pulmonary aneurysm is grave, e
specially in a fetus with intrauterine heart failure. Serial sonograph
ic follow-up is mandatory to detect the signs of hydrops fetalis. Earl
y intervention and intensive treatment should be given to improve the
perinatal outcome once the prenatal diagnosis is made.