Association of biliary atresia and urogenital sinus

A case of an association of extrahepatic biliary atresia (EHBA) and urogeni tal sinus (UGS) anomaly that was diagnosed as an urachal remnant antenatall y is reported. Diagnostic laparoscopy of the abdominal cavity in the postna tal period was the most helpful step for making the diagnosis. Biliary atre sia and urogenital sinus, which was the cause of bladder outlet obstruction , were treated successfully. To the authors' knowledge, this is the first c ase of this type of association introduced to the literature. Copyright (C) 2001 by W.B. Saunders Company.