Primary myxoma of the temporal bone in a 17-year-old boy: Case report

OBJECTIVE AND IMPORTANCE: Only two cases of primary intracranial myxomas ha ve been described previously in the literature: one patient had a primary i ntracranial myxoma in the pituitary fossa, and the other patient's myxoma w as located in the posterior fossa. CLINICAL PRESENTATION: A rave case of primary myxoma of the temporal bone i n a 17-year-old boy is described. The patient presented with a history of p rogressive left-sided hearing loss and increasing headaches of a few months ' duration. INTERVENTION: An initial draining procedure in the left ear revealed extant mucous material, and further investigation showed a large calcified lesion involving the petrous and temporal bones and filling the middle fossa. At surgery, a large mucoid-appearing tumor was removed. The tumor pathology re vealed a primary myxoma with bone and meningeal involvement. No clinical or histopathological evidence that it was a metastatic lesion was found. CONCLUSION: The features of myxomas on computed tomographic and magnetic re sonance imaging, the histopathology, and surgical considerations are discus sed.