Complex bronchopulmonary foregut malformation: extralobar pulmonary sequestration associated with a duplication cyst of mixed bronchogenic and oesophageal type

We report a 13-year-old girl with an unusual, complex bronchopulmonary fore gut malformation. The malformation included extralobar pulmonary sequestrat ion and a duplication cyst of mixed bronchogenic and oesophageal type. Preo perative CT and MRI demonstrated the cystic and solid portions of the mass and indicated an aberrant vascular supply, suggesting the possibility of br onchopulmonary foregut malformation and several other differential diagnose s. A direct communication between the cyst and the bronchus of the sequestr ated lung was found on pathological examination. This unusual combination o f an extralobar pulmonary sequestration and a foregut cyst points to a comm on embryological pathogenesis.