ODONTOGENIC MYXOMA IN AN ADOLESCENT WITH TUBEROUS SCLEROSIS

Tuberous sclerosis is a hamartoneoplastic syndrome characterised by ea rly onset of convulsive seizures with mental retardation. Oral abnorma lities, including enamel hypoplasia and mucosal fibromas, have been pr eviously reported. We report here a 17-year-old girl with this disorde r who had received repeated dental trauma. She presented with a swelli ng associated with a traumatised maxillary central incisor that sugges ted a diagnosis other than the odontogenic myxoma found at operation. Odontogenic myxoma has not previously been reported in this condition; it may represent an unusual phenotypic expression of the genetic defe ct understood to determine tuberous sclerosis, or it may be an unrelat ed coincidental finding.