Tongue-base hamartoma in tuberous sclerosis

This paper describes the case of a 41-year-old female with tuberous scleros is who persented with a large tongue-base hamartorna. The surgical manageme nt of the patient was complicated by the presence of a large thyroid goitre . Awake fibre-optic intubation, thyroidectomy then tracheostomy were necess ary before the tongue-base hamartoma could he safely resected. To the best of our knowledge, this is the first reported case of a tongue-base hamartom a in a patient with tuberous sclerosis.