Association between multiple intestinal atresia and omphalocele: A case report

Multiple intestinal atresia is a rare disorder with vascular or hereditary etiology. So far, the occurrence of this malformation along with omphalocel e has not been reported. We describe a boy born from a nonconsanguineous gy psy couple with intrauterine growth retardation, omphalocele, and multiple intestinal atresia from the pylorus to the rectum. The microscopic examinat ion of the intestine shows multiple small lumina with a sieve-like appearan ce. This is characteristic of the hereditary atresias and suggests developm ent of a defect in (re) canalization during embryogenesis. The association with omphalocele indicates a common developmental defect may be present.