Alpha 1-antitrypsin deficiency-associate panniculitis

Background: Hereditary alpha 1-antitrypsin deficiency may be very rarely as sociated with chronic panniculitis and is therefore often diagnosed only wi th delay. Case Report: The typical clinical features of the disease are described in a 37-year-old woman. This case underlines the importance of determining alp ha 1-antitrypsin levels in patients with chronic relapsing panniculitis. Th erapeutic approaches are discussed.