L. Marti et al., Perianal mucinous adenocarcinoma. Another reason for deep biopsy when dealing with anal fistulas or abscesses, CHIRURG, 72(5), 2001, pp. 573-577
A 39-year-old man came to us for surgical treatment of a hidradenitis suppu
rativa. Upon excision of a perianal abscess, the diagnosis of a rare tumor;
a perianal mucinous adenocarcinoma (pT4, pN 1, MO), was made. An abdominop
erineal resection was performed, followed by a combination of adjuvant radi
ation and chemotherapy. A year after the operation, the patient is doing we
ll without any signs of recurrence. This carcinoma probably arises in the a
nal glands. It often presents as a perirectal abscess and/or an anal fistul
a. Therefore, the diagnosis is often delayed. At presentation, the tumor is
bigger than 5 cm in diameter in 80 % of the cases, and the prognosis is po
or. It metastasizes mostly to the superficial inguinal or to the retrorecta
l lymph nodes. There are only ease reports and no comparative studies in th
e literature. In the last 10 years, the carcinoma has mostly been treated b
y neoadjuvant radiation and chemotherapy, followed by abdominoperineal rese
ction. Since then, the median survival has increased to 3 years. This is th
e first case report of a combination. of a perianal mucinous adenocarcinoma
with a hidradenitis suppurativa.