We report the case of a 7-year-old male child with a cystic tumour attached
to the caecum close to the ileocaecal valve. The histological examination
showed that the cyst had a ciliated epithelial lining, containing serous an
d mucous glands, with surrounding smooth muscle, inner circular and outer l
ongitudinal savers. The cyst was interpreted as an intestinal duplication l
ined with respiratory epithelium. This structure and its location, originat
ing from the midgut, is not in accordance with the typical conception of th
e embryogenesis. The clinical picture and treatment are described and compa
red to other findings in the literature.