We report on an 11-year-old girl with a large lymphangioma involving the lo
wer third of the abdominal wall, the mons pubis, both labia majora, the per
ianal region and extending into the pelvic bones. Because of an increasing
lymphorrhea from the cutaneous lesions resulting in considerable discomfort
and skin infections, the patient sought medical advice. After lymphologica
l check-up excluded the existence of a chylous reflux, the patient was pres
ented at a multidisciplinary medical council. A palliative surgical treatme
nt was recommended consisting of the resection of the most affected suprapu
bic region and the coverage of the resulting tissue defect with a gracilis
myocutaneous flap. Postoperatively, a venous stasis at the tip of the skin
paddle developed, which was relieved by the use of leeches and required sec
ondary closure. Despite these complications, the surgical intervention yiel
ded an acceptable cosmetic result, a diminution of lymphorrhea and hence su
bjectively some relief. Conclusion: Due to the variability of lymphangiomas
, an assessment by a multidisciplinary consultation is proposed. With respe
ct to therapy, the use of a myocutaneous flap represents one of the therape
utic options for large cutaneous lymphangiomas.