Congenital self-healing reticulohistiocytosis with eye involvement

Congenital self-healing reticulohistiocytosis (CSHR) represents the benign end of the spectrum of Langerhans cell histiocytoses, with spontaneous reso lution of lesions within the first year of life. However, Involvement of or gan systems other than the skin has been described occasionally and recurre nce of disease at sites distant from the skin has been documented. We repor t a case of CSHR with eye involvement that spontaneously resolved concurren t with resolution of skin lesions, Because multiple organ systems can be in volved and recurrences are possible, long-term follow-up of these patients is indicated.