The presentation of a neuroendocrine carcinoma in the paranasal sinuses is
extremely rare. Until now only 25 cases have been reported in the literatur
e. We report a case of 65-year-old male with an atypical carcinoid of the s
phenoid sinus which seemed to be associated with multiple endocrine neoplas
ia type 1 (MEN 1). To the best of our knowledge this is a first report on a
n atypical carcinoid in the sphenoid sinus.