An unusual spinal presentation of Whipple disease

When Whipple disease (WD) is confined to the CNS, diagnosis mag he difficul t. We report a case of WD with spinal presentation in an otherwise healthy woman who had a 5-year history of relapsing-remitting cervicothoracic myelo pathy. We suggest that the diagnosis of WD should be considered in the pres ence of an enlarged and enhancing spinal cord even in the absence of any sy stemic involvement.