Basal cell carcinoma (BCC) occurs rarely in children and is most often asso
ciated with an underlying condition that predisposes patients to the develo
pment of malignancy. There have been numerous reports of BCC developing aft
er puberty in nevus sebaceus; however, such occurrences have rarely been de
scribed in children. We report a 7-year-old boy with BCC forming in a nevus
sebaceus.