Endomyocardial fibrosis during Behcet's disease: A case report of a pseudo-tumoral form.

Citation
K. Belmadani et al., Endomyocardial fibrosis during Behcet's disease: A case report of a pseudo-tumoral form., ARCH MAL C, 94(4), 2001, pp. 282-286
Citations number
10
Categorie Soggetti
Cardiovascular & Respiratory Systems
Journal title
ARCHIVES DES MALADIES DU COEUR ET DES VAISSEAUX
ISSN journal
00039683 → ACNP
Volume
94
Issue
4
Year of publication
2001
Pages
282 - 286
Database
ISI
SICI code
0003-9683(200104)94:4<282:EFDBDA>2.0.ZU;2-R
Abstract
Endomyocardial fibrosis is very rare in Behcet's disease. The authors report the case of a 28 year old patient with Behcet's disease complicated by a pseudo-tumoral right ventricular formation on echocardiogr aphy. This misleading appearance suggested the diagnosis of cardiac thrombu s or tumour and led to a surgical approach which revealed a fibrous moderat or band suggesting endomyocardial fibrosis, confirmed by antomopathological analysis. Besides the originality of this case and the unusual pseudo-tumoral present ation, the authors underline the difficulties of establishing the diagnosis , despite the advances of medical imaging. The pseudo-tumoral intra-cardiac lesion in a suggestive clinical context (Behcet's disease) should raise su spicion of the diagnosis of endomyocardial fibrosis.