Endomyocardial fibrosis is very rare in Behcet's disease.
The authors report the case of a 28 year old patient with Behcet's disease
complicated by a pseudo-tumoral right ventricular formation on echocardiogr
aphy. This misleading appearance suggested the diagnosis of cardiac thrombu
s or tumour and led to a surgical approach which revealed a fibrous moderat
or band suggesting endomyocardial fibrosis, confirmed by antomopathological
analysis.
Besides the originality of this case and the unusual pseudo-tumoral present
ation, the authors underline the difficulties of establishing the diagnosis
, despite the advances of medical imaging. The pseudo-tumoral intra-cardiac
lesion in a suggestive clinical context (Behcet's disease) should raise su
spicion of the diagnosis of endomyocardial fibrosis.