Moyamoya syndrome is characterized by the reticulated collateralizatio
n of the intracranial vasculature distal to an occlusion of proximal i
ntracranial vessels. In the present study this pathology was visualize
d in 2 patients, aged 29 and 32 years, using transcranial color Dopple
r imaging (TCDI). Digital subtraction angiography in both patients rev
ealed stenosis of the intracranial portion of the internal carotid art
eries, occlusion and stenosis of several cerebral arteries, and a bila
teral reticulated collateral network particularly in the region of bot
h basal ganglia, typical of moyamoya syndrome. TCDI with power-mode Do
ppler depicted parts of the intracranial collateral network, not possi
ble using conventional color-flow Doppler. TCDI with power mode Dopple
r permitted better visualization of intracranial vascular pathology in
comparison to conventional color-flow Doppler, enabling a rapid and n
oninvasive diagnosis of rare cerebrovascular anomalies.