A 23-year-old, male patient previously operated on four times for a recurri
ng, benign, paranasal mass was admitted to our clinic with pain and swellin
g under the knee. Physical and radiological examination revealed a malignan
t process. The histopathological examination of the fine-needle biopsy spec
imen of the tibia was a malignant mixed tumor. Then, en-bloc resection, fre
e fibular grafting, and fixation with blade plate was performed for one-thi
rd of the tibia, conserving the knee joint. Recurrences and metastasis were
not observed after surgery and radiotherapy.