A young male with Marfan syndrome, diagnosed at the age of 10 years, presen
ted with conspicuous elongation and tortuosity of the internal carotid, mid
dle cerebral, vertebral and basilar arteries on cranial magnetic resonance
and computed tomography angiography. There is a little mention of cerebral
blood vessel examinations in the guidelines of the American Academy of Pedi
atrics for Marfan syndrome. Guidelines may be provided for the evaluation o
f cerebrovascular system for the patients with Marfan syndrome who have Fam
ily history of Marfan syndrome as well as a family history of death from su
barachinoid hemorrhage. (C) 2001 Elsevier Science B.V. All rights reserved.