Pyoderma vegetans (PV) is a chronic, vegetating pustular disorder character
ized clinically by erythematous vesiculopustular vegetating cutaneous plaqu
es. Marked epidermal hyperplasia, intraepidermal and subepidermal neutrophi
lic microabscesses and a dermal inflammatory infiltrate are the prominent h
istopathological findings. We describe a patient with PV associated with ul
cerative colitis and mammary Paget's disease. Pustular eruptions associated
with ulcerative colitis are reviewed.