A rare case of idiopathic midline destructive disease is presented, which i
s an entity of the so-called midline granuloma syndrome. Differentiation fr
om other granulomas, especially from Wegener's granulomatosis, is important
. This report shows the MR findings in a patient with atypical clinical pre
sentation of histopathologically proven idiopathic midline destructive dise
ase.