A. Ogose et al., Retroperitoneal malignant peripheral nerve sheath tumor associated with scoliosis in neurofibromatosis, J SPINAL D, 14(3), 2001, pp. 260-263
Neurofibromatosis 1 is an autosomal dominant disorder characterized by dist
inctive clinical problems including scoliosis and malignant peripheral nerv
e sheath tumors. We present two cases of retroperitoneal malignant peripher
al nerve sheath tumor associated with scoliosis in neurofibromatosis. Prese
nce of spinal deformity resulted in delay of the diagnosis of the sarcoma.