Hepatopulmonary syndrome consists of a triad of chronic liver disease, pulm
onary gas exchange abnormalities and pulmonary vascular dilatation in the a
bsence of detectable cardiopulmonary disease. Patients usually present with
symptoms of liver disease and the clinical recognition of this condition i
s a challenge. Newer non-invasive tests facilitate the diagnosis. Therapeut
ic strategies for this condition are still dismal. Liver transplantation is
a possible curative option for a subgroup of patients with hepatopulmonary
syndrome.