An 11-year total population study of Western Australia examined the prevale
nce and epidemiology of congenital upper limb anomalies. All anomalies were
classified according to the International Federation of Surgical Societies
of the Hand classification. We found the prevalence of babies born with up
per limb anomalies to be 1 in 506. Forty-six percent of those affected had
another nonhand congenital anomaly. Fifty-one percent had bilateral hand an
omalies, and 17% had multiple different hand anomalies. The most common ano
malies were failures of differentiation (35%), duplications (33%), and fail
ures of formation (15%). Congenital upper limb anomalies were more common i
n boys; preterm, postterm, and multiple births; and older mothers. No signi
ficant differences in prevalence or frequency of anomalies were found betwe
en whites and nonwhites, left and right sides, and in babies that survived
and those who died shortly after birth. Copyright (C) 2001 by the American
Society for Surgery of the Hand.