Introduction: Here we report the ninth case of pancreatoblastoma in an adul
t. Patient and method: At the time of diagnosis the female patient was 22 y
ears old. She had a tumor in the left upper abdomen, measuring 9 cm in diam
eter. Preoperatively the diagnosis of a pancreatoblastorna was suspected an
d an explorative laparotomy was performed followed by radical tumor extirpa
tion and intraoperative radiotherapy. After the diagnosis of a pancreatobla
stoma was confirmed by definitive histopathological examination, combined R
adiochemotherapy was performed. Discussion: Special features in histomorpho
logical characterization of the tumor and problems concerning diagnosis and
differential diagnosis as well as the lack of a definitive therapy regime
are discussed.