Background. Intramedullary neurosarcoidosis may be the first manifestation
of the disease and may mimic a tumor clinically and radiographically. Two p
atients who presented: with cervical intramedullary lesions on magnetic res
onance imaging: (MRI) scans were found to have neurosarcoidosis. Clinical p
resentation. Two patients with negative past medical history presented with
progressive myelopathic features, and intramedullary cervical lesions were
detected on MRI scan; the diagnosis was made on biopsy of the lesions. Ear
ly therapeutic intervention ted to a favorable outcome. Conclusion. Infra-m
edullary neurosarcoidosis, especially in the cervical cord, can be the init
ial presentation of the disease, mimicking a tumor, MRI scan, biopsy, and,
in: fewer cases, angiotensin-converting enzyme levels can help with the dia
gnosis and may lead to a favorable outcome.