Papular acantholytic dyskeratosis of the vulva

We describe two patients with unusual asymptomatic, papular lesions on the vulva, clinically resembling lichen planus, the histology of which revealed unexpected findings of suprabasilar clefting, acantholysis and dyskeratoti c cells giving rise to corps ronds and grains together with hyperkeratosis and parakeratosis. features originally associated with a diagnosis of Darie r's disease. Focal acantholytic dyskeratosis has been described in a wide v ariety of inflammatory and neoplastic processes including those involving m ucous membranes and has been attributed various diagnostic labels. We feel that the findings in our patients are consistent with a diagnosis of papula r acantholytic dyskeratosis of the vulva, a rare condition, which was first described in 1984.