Idiopathic granulomatous mastitis is a very rare benign breast disease, whi
ch mimics breast cancer both clinically and mammographically. Most cases ha
ve an unknown aetiology, however, we found an alpha-I-antitrypsin deficienc
y. A literature review is presented and the controversies in diagnosis and
management are discussed. (C) 2001 Elsevier Science Ireland Ltd. All rights
reserved.