Adult extrarenal wilms tumor occurring in the uterus - A case report and review of the literature

Five previous cases of extrarenal Wilms tumor (EWT) occurring in the uterus have been reported. The oldest patient was 22 years. We report a case of u terine EWT occurring in a 42-year-old woman. Histologically, there was typi cal triphasic differentiation, including epithelial, blastemal, and mesench ymal elements. The important differential diagnosis in this age group, the malignant mixed mullerian tumor, is excluded by the absence of glomeruloid structures and primitive tubules. The exact histogenesis of EWT is unknown but most likely relates to the presence of nephrogenic rests occurring in t he female genital tract.