Autoimmune pancreatitis is a relatively rare type of chronic pancreatitis t
hat may be associated with other autoimmune disorders. The imaging features
of this entity may be misleading and suggest the presence of a malignant t
umour. We present a case in which MR imaging allowed us to diagnose autoimm
une pancreatitis associated with primary sclerosing cholangitis, which is a
nother autoimmune-related disease. Typical MR characteristics of autoimmune
pancreatitis include focal or diffuse enlargement of the pancreas, the abs
ence of parenchymal atrophy and significant dilation proximal to the site o
f stenosis, the absence of peripancreatic spread, the clear demarcation of
the lesion and the presence of a peripancreatic rim.