We report the case of a conjunctival tumor in a 9-year-old patient, sufferi
ng from Xeroderma Pigmentosum. Our patient presented a raspberry-colored co
njunctival tumor. The tumor was resecked without any additional treatment.
The histological study revealed squamous cell carcinoma. A suspicion of rel
apse appeared two months later of the same location and a new resection was
performed. The initial checkup of this tumor was negative.
In this disease, ocular localizations are frequent. The conjunctiva, the co
rnea, the eyelids and, into a lesser extent, the orbit can be involved. Bas
al cell carcinoma and squamous cell carcinoma are the most frequent tumors
observed in Xeroderma Pigmentosum. Their treatment is mainly surgical.