Congenital pulmonary lymphangiectasia: A case report of thoracic duct agenesis

Authors
Antonetti, M Manuck, TA Schramm, C Hight, D
Citation
M. Antonetti et al., Congenital pulmonary lymphangiectasia: A case report of thoracic duct agenesis, PEDIAT PULM, 32(2), 2001, pp. 184-186
Citations number
12
Categorie Soggetti
Pediatrics
Journal title
PEDIATRIC PULMONOLOGY
ISSN journal
87556863 → ACNP
Volume
32
Issue
2
Year of publication
2001
Pages
184 - 186
Database
ISI
SICI code
8755-6863(200108)32:2<184:CPLACR>2.0.ZU;2-0
Abstract
We present a 17-year-old Caucasian male with congenital pulmonary lymphangi ectasia and an absent thoracic duct. This patient is unique as he did not p resent with the disorder until age 9.5 years. Since his initial presentatio n he has had recurrent chylothoraces and has been treated symptomatically. We discuss the possible implications of his disorder as well as some of the limited treatment that is available. (C) 2001 Wiley-Liss, Inc.