Intramural hematomas (IMH) are regarded as a hemorrhage into the aortic wal
l. In general a traumatic form can de differentiated from a spontaneous non
-traumatic. There is a predisposition of IMH with arterial hypertension and
mesoectodermal dysplastic syndromes. The diagnosis is established with the
clinical presentation in combination with the findings of different imagin
g modalities. Acute and subacute discomfort associated with a tendency of c
ollaps are considered as typical presenting complaints. A semicircular or c
oncentric thickening of the aortic wall with the absence of blood flow or a
dissection membran are typical findings in transesophageal echocardiograph
y, computed tomography and magnetic resonance tomography. From a differenti
al diagnostic point of view a distinction from atherosclerotic wall changes
, intraluminal thrombi and inflammatory aortic diseases is essential. The I
MH is considered as an early presentation of aortic dissection, put into an
d treated according to the Stanford classification. In the course of natura
l history an IMH can disappear, rupture or progress into a classic aortic d
issection.